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1. 2.6.1.42 enzyme   branched-chain aminotransferase
                      branched-chain amino acid aminotransferase
                      branched-chain-amino-acid transaminase
                      L-branched chain amino acid aminotransferase
                      branched-chain amino acid-glutamate transaminase
                      glutamate-branched-chain amino acid transaminase
                      branched-chain-amino-acid:2-oxoglutarate aminotransferase
                      transaminase B

2. 3.1.2.19 enzyme   medium-chain hydrolase
                      medium-chain acyl-CoA hydrolase
                      medium-chain acyl-thioester hydrolase
                      medium-chain acyl coenzyme A hydrolase
                      ADP-dependent medium-chain-acyl-CoA hydrolase
                      ADP-dependent-medium-chain-acyl-CoA hydrolase
                      myristoyl-CoA thioesterase

3. 3.5.1.55 enzyme   long-chain aminoacylase
                      long-chain acylglutamate amidase
                      long-chain-fatty-acyl-glutamate deacylase
                      N-long-chain-fatty-acyl-L-glutamate amidohydrolase
                      N-acyl-D-glutamate deacylase

4. 1.13.99.3 enzyme   tryptophan side chain oxidase
                      tryptophan side-chain oxidase
                      tryptophan side chain oxidase II
                      tryptophan side chain oxidase type I
                      tryptophan side-chain alpha,beta-oxidase
                      L-tryptophan:oxygen 2'-oxidoreductase (side-chain-cleaving)
                      TSO
                      TSO I
                      TSO II
                      tryptophan 2'-dioxygenase
                      indole-3-alkane alpha-hydroxylase
                      indolyl-3-alkan alpha-hydroxylase

5. 1.14.15.6 enzyme   C27-side chain cleavage enzyme
                      cholesterol monooxygenase (side-chain-cleaving)
                      cholesterol side-chain cleavage enzyme
                      cholesterol side-chain-cleaving enzyme
                      enzymes, cholesterol side-chain-cleaving
                      cholesterol,reduced-adrenal-ferredoxin:oxygen oxidoreductase (side-chain-cleaving)
                      cholesterol desmolase
                      cytochrome P-450scc
                      cholesterol 20-22-desmolase
                      cholesterol C20-22 desmolase
                      desmolase, steroid 20-22
                      steroid 20-22 desmolase
                      steroid 20-22-lyase

6. 1.1.1.192 enzyme   long-chain alcohol dehydrogenase
                      long-chain-alcohol dehydrogenase
                      long-chain-alcohol:NAD+ oxidoreductase
                      fatty alcohol oxidoreductase

7. 1.1.3.20 enzyme   long-chain-alcohol oxidase
                      long-chain fatty acid oxidase
                      long-chain fatty alcohol oxidase
                      long-chain-alcohol:oxygen oxidoreductase
                      fatty alcohol oxidase
                      fatty alcohol:oxygen oxidoreductase

8. 1.2.1.48 enzyme   long-chain-aldehyde dehydrogenase
                      long-chain aliphatic aldehyde dehydrogenase
                      long-chain fatty aldehyde dehydrogenase
                      long-chain-aldehyde:NAD+ oxidoreductase
                      fatty aldehyde:NAD+ oxidoreductase

9. 1.2.4.4 enzyme   branched-chain ketoacid dehydrogenase
                      branched chain keto acid dehydrogenase
                      branched-chain keto acid dehydrogenase
                      branched-chain (-2-oxoacid) dehydrogenase (BCD)
                      branched-chain 2-keto acid dehydrogenase
                      branched-chain 2-oxo acid dehydrogenase
                      branched-chain alpha-keto acid dehydrogenase
                      branched-chain alpha-oxo acid dehydrogenase
                      dehydrogenase, branched chain alpha-keto acid
                      BCKDH
                      BCOAD
                      2-oxoisocaproate dehydrogenase
                      alpha-ketoisocaproate dehydrogenase
                      alpha-ketoisocaproic dehydrogenase
                      alpha-ketoisovalerate dehydrogenase
                      alpha-oxoisocaproate dehydrogenase
                      2-oxoisovalerate (lipoate) dehydrogenase
                      dehydrogenase, 2-oxoisovalerate (lipoate)
                      alpha-keto-alpha-methylvalerate dehydrogenase
                      3-methyl-2-oxobutanoate dehydrogenase (lipoamide)
                      alpha-ketoisocaproic-alpha-keto-alpha-methylvaleric dehydrogenase
                      3-methyl-2-oxobutanoate dehydrogenase  (2-methylpropanoyl-transferring)
                      3-methyl-2-oxobutanoate:lipoamide oxidoreductase (decarboxylating  and acceptor-2-methylpropanoylating)
                      3-methyl-2-oxobutanoate:[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase]-lipoyllysine 2-oxidoreductase (decarboxylating, acceptor-2-methylpropanoylating)

10. 1.6.5.3 enzyme   complex I (electron transport chain)
                      ubiquinone reductase
                      DPNH-ubiquinone reductase
                      NADH dehydrogenase (ubiquinone)
                      NADH-CoQ oxidoreductase
                      NADH-CoQ reductase
                      NADH-Q6 oxidoreductase
                      NADH-ubiquinone oxidoreductase
                      NADH-ubiquinone reductase
                      NADH2 dehydrogenase (ubiquinone)
                      NADH:ubiquinone oxidoreductase
                      coenzyme Q reductase
                      complex 1 dehydrogenase
                      type 1 dehydrogenase
                      DPNH-coenzyme Q reductase
                      NADH coenzyme Q1 reductase
                      NADH-coenzyme Q oxidoreductase
                      NADH-coenzyme Q reductase
                      NADH-ubiquinone-1 reductase
                      NADH:ubiquinone oxidoreductase complex
                      electron transfer complex I
                      complex I (NADH:Q1 oxidoreductase)
                      complex I (mitochondrial electron transport)
                      mitochondrial electron transport complex 1
                      mitochondrial electron transport complex I
                      dihydronicotinamide adenine dinucleotide-coenzyme Q reductase
                      reduced nicotinamide adenine dinucleotide-coenzyme Q reductase

11. 2.3.1.137 enzyme   carnitine medium-chain acyltransferase
                      medium-chain/long-chain carnitine acyltransferase
                      carnitine O-octanoyltransferase
                      overt mitochondrial carnitine palmitoyltransferase
                      easily solubilized mitochondrial carnitine palmitoyltransferase
                      octanoyl-CoA:L-carnitine O-octanoyltransferase

12. 2.7.11.18 enzyme   [myosin-light-chain] kinase
                      myosin light chain kinase
                      myosin-light-chain kinase
                      myosin light chain protein kinase
                      myosin light-chain kinase (phosphorylating)
                      ATP:myosin-light-chain O-phosphotransferase
                      smooth-muscle-myosin-light-chain kinase
                      calcium/calmodulin-dependent myosin light chain kinase
                      MLCK
                      MLCKase
                      STK18
                      myosin kinase

13. 2.7.1.117 enzyme   myosin-light-chain kinase
                      myosin light chain protein kinase
                      myosin light-chain kinase (phosphorylating)
                      ATP:[myosin-light-chain] O-phosphotransferase
                      ATP:myosin-light-chain O-phosphotransferase
                      smooth-muscle-myosin-light-chain kinase
                      calcium/calmodulin-dependent myosin light chain kinase
                      myosin kinase

14. 2.7.1.129 enzyme   [myosin-heavy-chain] kinase
                      myosin-heavy-chain kinase
                      ATP:[myosin-heavy-chain] O-phosphotransferase
                      ATP:myosin-heavy-chain O-phosphotransferase

15. 3.1.3.53 enzyme   [myosin-light-chain] phosphatase
                      myosin-light-chain-phosphatase
                      [myosin-light-chain]-phosphate phosphohydrolase
                      myosin light chain kinase phosphatase
                      myosin phosphatase
                      protein phosphatase 2A

16. 4.1.1.72 enzyme   branched-chain keto acid decarboxylase
                      branched-chain oxo acid decarboxylase
                      branched-chain-2-oxoacid decarboxylase
                      branched-chain alpha-keto acid decarboxylase
                      BCKA
                      (3S)-3-methyl-2-oxopentanoate carboxy-lyase

17. 5.3.1.21 enzyme   corticosteroid side-chain-isomerase
                      11-deoxycorticosterone ketol-isomerase
                      11-deoxycorticosterone aldose-ketose-isomerase

18. 1.11.1.3 enzyme   long chain fatty acid peroxidase
                      fatty-acid peroxidase
                      hexadecanoate:hydrogen-peroxide oxidoreductase

19. 1.1.1.211 enzyme   long-chain-3-hydroxyacyl-CoA dehydrogenase
                      long-chain 3-hydroxyacyl coenzyme A dehydrogenase
                      long-chain-(S)-3-hydroxyacyl-CoA:NAD+ oxidoreductase
                      LCHAD
                      3-hydroxyacyl-CoA dehydrogenase
                      beta-hydroxyacyl-CoA dehydrogenase

20. 1.2.7.7 enzyme   branched-chain ketoacid ferredoxin reductase
                      branched-chain oxo acid ferredoxin reductase
                      VOR
                      ketoisovalerate ferredoxin reductase
                      2-ketoisovalerate ferredoxin reductase
                      2-oxoisovalerate ferredoxin reductase
                      keto-valine-ferredoxin oxidoreductase
                      3-methyl-2-oxobutanoate dehydrogenase (ferredoxin)
                      3-methyl-2-oxobutanoate synthase (ferredoxin)
                      3-methyl-2-oxobutanoate:ferredoxin oxidoreductase (decarboxylating; CoA-2-methylpropanoylating)

21. 1.3.99.12 enzyme   branched-chain acyl-CoA dehydrogenase
                      2-methyl branched chain acyl-CoA dehydrogenase
                      2-methylacyl-CoA dehydrogenase
                      2-methylbutanoyl-CoA:(acceptor) oxidoreductase

22. 1.3.99.13 enzyme   long-chain-acyl-CoA dehydrogenase
                      long-chain acyl-coenzyme A dehydrogenase
                      long-chain-acyl-CoA:(acceptor) 2,3-oxidoreductase
                      palmitoyl-CoA dehydrogenase
                      palmitoyl-coenzyme A dehydrogenase

23. 1.3.99.2 enzyme   short-chain acyl CoA dehydrogenase
                      short-chain acyl-coenzyme A dehydrogenase
                      butyryl dehydrogenase
                      ethylene reductase
                      butyryl-CoA dehydrogenase
                      3-hydroxyacyl CoA reductase
                      butyryl coenzyme A dehydrogenase
                      enoyl-coenzyme A reductase
                      unsaturated acyl-CoA reductase
                      unsaturated acyl coenzyme A reductase
                      butanoyl-CoA:(acceptor) 2,3-oxidoreductase

24. 1.3.99.3 enzyme   long-chain acyl-CoA dehydrogenase
                      medium-chain acyl-CoA dehydrogenase
                      long-chain acyl coenzyme A dehydrogenase
                      medium-chain acyl-coenzyme A dehydrogenase
                      acyl dehydrogenase
                      acyl CoA dehydrogenase
                      acyl-CoA dehydrogenase
                      acyl coenzyme A dehydrogenase
                      fatty-acyl-CoA dehydrogenase
                      general acyl CoA dehydrogenase
                      fatty acyl coenzyme A dehydrogenase
                      acyl-CoA:(acceptor) 2,3-oxidoreductase

25. 2.3.1.16 enzyme   long-chain 3-oxoacyl-CoA thiolase
                      KAT
                      3-ketothiolase
                      beta-ketothiolase
                      thiolase I
                      3-ketoacyl thiolase
                      acetyl-CoA acyltransferase
                      ketoacyl-CoA acyltransferase
                      3-ketoacyl CoA thiolase
                      3-ketoacyl-CoA thiolase
                      3-oxoacyl-CoA thiolase
                      6-oxoacyl-CoA thiolase
                      acetoacetyl-CoA beta-ketothiolase
                      acetyl-CoA C-acyltransferase
                      beta-ketoacyl-CoA thiolase
                      beta-ketoadipyl-CoA thiolase
                      ketoacyl-coenzyme A thiolase
                      oxoacyl-coenzyme A thiolase
                      2-methylacetoacetyl-CoA thiolase [misleading]
                      3-ketoacyl coenzyme A thiolase
                      3-oxoacyl-coenzyme A thiolase
                      beta-ketoacyl coenzyme A thiolase
                      beta-ketoadipyl coenzyme A thiolase
                      pro-3-ketoacyl-CoA thiolase
                      acyl-CoA:acetyl-CoA C-acyltransferase

26. 2.3.1.75 enzyme   long-chain-alcohol O-fatty-acyltransferase
                      acyl-CoA:long-chain-alcohol O-acyltransferase
                      wax synthase
                      wax-ester synthase

27. 2.7.2.14 enzyme   branched-chain-fatty-acid kinase
                      ATP:branched-chain-fatty-acid 1-phosphotransferase
                      isobutyrate kinase

28. 3.1.1.28 enzyme   long-chain acyl-L-carnitine hydrolase
                      HACH
                      acylcarnitine hydrolase
                      palmitoylcarnitine hydrolase
                      O-acylcarnitine acylhydrolase
                      carnitine ester hydrolase
                      palmitoyl carnitine hydrolase
                      high activity acylcarnitine hydrolase
                      palmitoyl-L-carnitine hydrolase

29. 3.1.2.18 enzyme   short-chain acyl-CoA hydrolase
                      short-chain acyl-CoA thioesterase
                      short-chain acyl coenzyme A hydrolase
                      ADP-dependent short-chain-acyl-CoA hydrolase
                      ADP-dependent-short-chain-acyl-CoA hydrolase
                      propionyl-CoA hydrolase
                      propionyl-CoA thioesterase
                      propionyl coenzyme A hydrolase

30. 3.5.1.60 enzyme   N-(long-chain-acyl)ethanolamine amidohydrolase
                      N-(long-chain-acyl)ethanolamine deacylase
                      acylethanolamine amidase
                      N-acylethanolamine amidohydrolase

31. 4.2.1.17 enzyme   short-chain enoyl-CoA hydratase
                      short chain enoyl coenzyme A hydratase
                      ECH
                      crotonase
                      crotonyl hydrase
                      enoyl hydrase
                      beta-hydroxyacid dehydrase
                      enol-CoA hydratase
                      enoyl-CoA hydratase
                      2-enoyl-CoA hydratase
                      acyl coenzyme A hydrase
                      beta-hydroxyacyl-CoA dehydrase
                      enoyl coenzyme A hydratase
                      hydratase, enoyl coenzyme A
                      unsaturated acyl-CoA hydratase
                      2-octenoyl coenzyme A hydrase
                      D-3-hydroxyacyl-CoA dehydratase
                      enoyl coenzyme A hydrase (D)
                      enoyl coenzyme A hydrase (L)
                      trans-2-enoyl-CoA hydratase
                      (3S)-3-hydroxyacyl-CoA hydro-lyase

32. 4.2.1.74 enzyme   long-chain-enoyl-CoA hydratase
                      long-chain enoyl coenzyme A hydratase
                      long-chain-(3S)-3-hydroxyacyl-CoA hydro-lyase

33. 6.2.1.1 enzyme   short chain fatty acyl-CoA synthetase
                      short-chain acyl-coenzyme A synthetase
                      ACS
                      acetate thiokinase
                      acetic thiokinase
                      acetate-CoA ligase
                      acetyl CoA ligase
                      acetyl CoA synthase
                      acetyl activating enzyme
                      acetyl-CoA synthetase
                      acyl-activating enzyme
                      acetyl coenzyme A synthetase
                      acetyl-coenzyme A synthase
                      acetate:CoA ligase (AMP-forming)

34. 6.2.1.2 enzyme   fatty acid thiokinase (medium chain)
                      medium chain acyl-CoA synthetase
                      short-chain acyl-CoA synthetase
                      acyl-activating enzyme
                      butyrate-CoA ligase
                      butyryl-CoA synthetase
                      fatty acid elongase
                      butyryl-coenzyme A synthetase
                      fatty acid activating enzyme
                      L-(+)-3-hydroxybutyryl CoA ligase
                      butanoate:CoA ligase (AMP-forming)
                      fatty acyl coenzyme A synthetase

35. 6.2.1.3 enzyme   fatty acid thiokinase (long chain)
                      long-chain acyl CoA synthetase
                      long chain fatty acyl-CoA synthetase
                      long-chain acyl-CoA synthetase I
                      long-chain acyl-CoA synthetase II
                      long-chain acyl-coenzyme A synthetase
                      long-chain-fatty-acid-CoA ligase
                      long-chain fatty acyl coenzyme A synthetase
                      ACS3
                      FAA1
                      thiokinase
                      LCFA synthetase
                      acyl-CoA ligase
                      acyl-CoA synthetase
                      acyl-activating enzyme
                      arachidonyl-CoA synthetase
                      fatty acid elongase
                      lignoceroyl-CoA synthase
                      oleoyl-CoA synthetase
                      palmitoyl-CoA ligase
                      palmitoyl-CoA synthase
                      pristanoyl-CoA synthetase
                      stearoyl-CoA synthetase
                      acyl coenzyme A synthetase
                      acyl-coenzyme A ligase
                      fatty acid CoA ligase
                      palmitoyl coenzyme A synthetase
                      acid:CoA ligase (AMP-forming)
                      fatty acyl-coenzyme A synthetase

36. 1.14.19.3 enzyme   long-chain fatty acid delta6-desaturase
                      delta6-desaturase
                      linoleate desaturase
                      linoleic desaturase
                      linoleic acid desaturase
                      linoleoyl CoA desaturase
                      linoleoyl-CoA desaturase
                      delta6-acyl CoA desaturase
                      fatty acid 6-desaturase
                      fatty acid delta6-desaturase
                      linoleoyl-coenzyme A desaturase
                      delta6-fatty acyl-CoA desaturase
                      linoleoyl-CoA,hydrogen-donor:oxygen oxidoreductase

37. 1.2.1.50 enzyme   long-chain-fatty-acyl-CoA reductase
                      long-chain-aldehyde:NADP+ oxidoreductase (acyl-CoA-forming)
                      acyl-CoA reductase
                      acyl coenzyme A reductase

38. 1.3.1.52 enzyme   2-methyl-branched-chain-enoyl-CoA reductase
                      2-methyl-branched-chain-acyl-CoA:NAD+ 2-oxidoreductase

39. 2.7.1.115 enzyme   branched-chain alpha-ketoacid dehydrogenase kinase
                      branched-chain keto acid dehydrogenase kinase
                      branched-chain 2-oxo acid dehydrogenase kinase
                      branched-chain oxo acid dehydrogenase kinase (phosphorylating)
                      [3-methyl-2-oxobutanoate dehydrogenase (lipoamide)] kinase
                      ATP:[3-methyl-2-oxobutanoate dehydrogenase (lipoamide)] phosphotransferase

40. 3.1.2.2 enzyme   long-chain fatty-acyl-CoA hydrolase
                      palmitoyl thioesterase
                      palmityl thioesterase
                      palmitoyl-CoA deacylase
                      palmitoyl-CoA hydrolase
                      palmitoyl-CoA hydrolase
                      palmityl thioesterase I
                      palmityl-CoA deacylase
                      fatty acyl thioesterase I
                      palmitoyl coenzyme A hydrolase

41. 3.1.3.52 enzyme   branched-chain oxo-acid dehydrogenase phosphatase
                      branched-chain 2-keto acid dehydrogenase phosphatase
                      branched-chain alpha-keto acid dehydrogenase phosphatase
                      BCKDH
                      [3-methyl-2-oxobutanoate dehydrogenase (lipoamide)]-phosphatase
                      [3-methyl-2-oxobutanoate dehydrogenase (lipoamide)]-phosphate phosphohydrolase

42. 3.4.21.73 enzyme   double-chain urokinase-type plasminogen activator
                      two-chain urokinase-type plasminogen activator
                      abbokinase
                      uPA
                      urokinase
                      u-PA
                      cellular plasminogen activator
                      u-plasminogen activator
                      urinary esterase A
                      urinary plasminogen activator
                      urokinase plasminogen activator
                      urokinase-type plasminogen activator

43. 1.1.1.36 enzyme   short chain beta-ketoacetyl(acetoacetyl)-CoA reductase
                      acetoacetyl-CoA reductase
                      NADPH:acetoacetyl-CoA reductase
                      acetoacetyl coenzyme A reductase
                      beta-ketoacyl-CoA reductase
                      hydroxyacyl coenzyme-A dehydrogenase
                      (R)-3-hydroxyacyl-CoA dehydrogenase
                      D-3-hydroxyacyl-CoA reductase
                      NADP-linked acetoacetyl CoA reductase
                      (R)-3-hydroxyacyl-CoA:NADP+ oxidoreductase
                      D(-)-beta-hydroxybutyryl CoA-NADP oxidoreductase

44. 3.1.1.67 enzyme   long-chain-fatty-acyl-ethyl-ester acylhydrolase
                      FAEES
                      fatty-acyl-ethyl-ester synthase

45. 3.1.3.16 enzyme   branched-chain alpha-keto acid dehydrogenase phosphatase
                      calcineurin
                      BCKDH phosphatase
                      casein phosphatase
                      phosphatase 2A
                      phosphatase 2B
                      phosphatase I
                      phosphatase IB
                      phosphatase II
                      phosphatase III
                      phosphatase IV
                      phosphatase SP
                      phosphoprotein phosphatase
                      phosphoprotein phosphohydrolase
                      phosphospectrin phosphatase
                      protein phosphatase
                      phosphatase C-II
                      phosphatase H-II
                      phosphopyruvate dehydrogenase phosphatase
                      protein D phosphatase
                      protein phosphatase-1
                      protein phosphatase-2A
                      protein phosphatase-2B
                      protein phosphatase-2C
                      HMG-CoA reductase phosphatase
                      polycation modulated (PCM-) phosphatase
                      Aspergillus awamori acid protein phosphatase
                      3-hydroxy 3-methylglutaryl coenzymeA reductase phosphatase

46. 6.2.1.19 enzyme   long-chain-fatty-acid-luciferin-component ligase
                      long-chain-fatty-acid:protein ligase (AMP-forming)
                      acyl-protein synthetase

47. 2.5.1.26 enzyme   1-acyl-glycerone-3-phosphate:long-chain-alcohol O-3-phospho-2-oxopropanyltransferase
                      DHAP-AT
                      alkyl-DHAP
                      alkyldihydroxyacetonephosphate synthase
                      alkyl DHAP synthetase
                      alkyldihydroxyacetone phosphate synthetase
                      alkylglycerone-phosphate synthase
                      dihydroxyacetone-phosphate acyltransferase

48. 6.2.1.20 enzyme   long-chain-fatty-acid-[acyl-carrier-protein] ligase
                      long-chain-fatty-acid:[acyl-carrier-protein] ligase (AMP-forming)
                      acyl-ACP synthetase
                      stearoyl-ACP synthetase
                      acyl-[acyl carrier protein] synthetase
                      acyl-[acyl-carrier-protein] synthetase
                      acyl-[acyl-carrier-protein]synthetase
                      acyl-acyl carrier protein synthetase

49. 1.14.13.54 enzyme   17alpha-hydroxyprogesterone, NADPH2:oxygen oxidoreductase  (20-hydroxylating, side-chain cleaving)
                      ketosteroid,NADPH:oxygen oxidoreductase (20-hydroxylating, ester-producing/20-hydroxylating, side-chain cleaving/17-hydroxylating, lactonizing)
                      ketosteroid monooxygenase
                      steroid-ketone monooxygenase
                      androstenedione, NADPH2:oxygen oxidoreductase (17-hydroxylating,  lactonizing)
                      progesterone, NADPH2:oxygen oxidoreductase (20-hydroxylating,  ester-producing)


BiSSCat v1.06.20 http://bisscat.org/
Developed by Masaaki Kotera, Department of Biochemistry, Trinity College Dublin.
Science Foundation of Ireland is gratefully acknowledged.