1. 2.6.1.42 enzyme branched-chain aminotransferase
branched-chain amino acid aminotransferase
branched-chain-amino-acid transaminase
L-branched chain amino acid aminotransferase
branched-chain amino acid-glutamate transaminase
glutamate-branched-chain amino acid transaminase
branched-chain-amino-acid:2-oxoglutarate aminotransferase
transaminase B
2. 3.1.2.19 enzyme medium-chain hydrolase
medium-chain acyl-CoA hydrolase
medium-chain acyl-thioester hydrolase
medium-chain acyl coenzyme A hydrolase
ADP-dependent medium-chain-acyl-CoA hydrolase
ADP-dependent-medium-chain-acyl-CoA hydrolase
myristoyl-CoA thioesterase
3. 3.5.1.55 enzyme long-chain aminoacylase
long-chain acylglutamate amidase
long-chain-fatty-acyl-glutamate deacylase
N-long-chain-fatty-acyl-L-glutamate amidohydrolase
N-acyl-D-glutamate deacylase
4. 1.13.99.3 enzyme tryptophan side chain oxidase
tryptophan side-chain oxidase
tryptophan side chain oxidase II
tryptophan side chain oxidase type I
tryptophan side-chain alpha,beta-oxidase
L-tryptophan:oxygen 2'-oxidoreductase (side-chain-cleaving)
TSO
TSO I
TSO II
tryptophan 2'-dioxygenase
indole-3-alkane alpha-hydroxylase
indolyl-3-alkan alpha-hydroxylase
5. 1.14.15.6 enzyme C27-side chain cleavage enzyme
cholesterol monooxygenase (side-chain-cleaving)
cholesterol side-chain cleavage enzyme
cholesterol side-chain-cleaving enzyme
enzymes, cholesterol side-chain-cleaving
cholesterol,reduced-adrenal-ferredoxin:oxygen oxidoreductase (side-chain-cleaving)
cholesterol desmolase
cytochrome P-450scc
cholesterol 20-22-desmolase
cholesterol C20-22 desmolase
desmolase, steroid 20-22
steroid 20-22 desmolase
steroid 20-22-lyase
6. 1.1.1.192 enzyme long-chain alcohol dehydrogenase
long-chain-alcohol dehydrogenase
long-chain-alcohol:NAD+ oxidoreductase
fatty alcohol oxidoreductase
7. 1.1.3.20 enzyme long-chain-alcohol oxidase
long-chain fatty acid oxidase
long-chain fatty alcohol oxidase
long-chain-alcohol:oxygen oxidoreductase
fatty alcohol oxidase
fatty alcohol:oxygen oxidoreductase
8. 1.2.1.48 enzyme long-chain-aldehyde dehydrogenase
long-chain aliphatic aldehyde dehydrogenase
long-chain fatty aldehyde dehydrogenase
long-chain-aldehyde:NAD+ oxidoreductase
fatty aldehyde:NAD+ oxidoreductase
9. 1.2.4.4 enzyme branched-chain ketoacid dehydrogenase
branched chain keto acid dehydrogenase
branched-chain keto acid dehydrogenase
branched-chain (-2-oxoacid) dehydrogenase (BCD)
branched-chain 2-keto acid dehydrogenase
branched-chain 2-oxo acid dehydrogenase
branched-chain alpha-keto acid dehydrogenase
branched-chain alpha-oxo acid dehydrogenase
dehydrogenase, branched chain alpha-keto acid
BCKDH
BCOAD
2-oxoisocaproate dehydrogenase
alpha-ketoisocaproate dehydrogenase
alpha-ketoisocaproic dehydrogenase
alpha-ketoisovalerate dehydrogenase
alpha-oxoisocaproate dehydrogenase
2-oxoisovalerate (lipoate) dehydrogenase
dehydrogenase, 2-oxoisovalerate (lipoate)
alpha-keto-alpha-methylvalerate dehydrogenase
3-methyl-2-oxobutanoate dehydrogenase (lipoamide)
alpha-ketoisocaproic-alpha-keto-alpha-methylvaleric dehydrogenase
3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
3-methyl-2-oxobutanoate:lipoamide oxidoreductase (decarboxylating and acceptor-2-methylpropanoylating)
3-methyl-2-oxobutanoate:[dihydrolipoyllysine-residue (2-methylpropanoyl)transferase]-lipoyllysine 2-oxidoreductase (decarboxylating, acceptor-2-methylpropanoylating)
10. 1.6.5.3 enzyme complex I (electron transport chain)
ubiquinone reductase
DPNH-ubiquinone reductase
NADH dehydrogenase (ubiquinone)
NADH-CoQ oxidoreductase
NADH-CoQ reductase
NADH-Q6 oxidoreductase
NADH-ubiquinone oxidoreductase
NADH-ubiquinone reductase
NADH2 dehydrogenase (ubiquinone)
NADH:ubiquinone oxidoreductase
coenzyme Q reductase
complex 1 dehydrogenase
type 1 dehydrogenase
DPNH-coenzyme Q reductase
NADH coenzyme Q1 reductase
NADH-coenzyme Q oxidoreductase
NADH-coenzyme Q reductase
NADH-ubiquinone-1 reductase
NADH:ubiquinone oxidoreductase complex
electron transfer complex I
complex I (NADH:Q1 oxidoreductase)
complex I (mitochondrial electron transport)
mitochondrial electron transport complex 1
mitochondrial electron transport complex I
dihydronicotinamide adenine dinucleotide-coenzyme Q reductase
reduced nicotinamide adenine dinucleotide-coenzyme Q reductase
11. 2.3.1.137 enzyme carnitine medium-chain acyltransferase
medium-chain/long-chain carnitine acyltransferase
carnitine O-octanoyltransferase
overt mitochondrial carnitine palmitoyltransferase
easily solubilized mitochondrial carnitine palmitoyltransferase
octanoyl-CoA:L-carnitine O-octanoyltransferase
12. 2.7.11.18 enzyme [myosin-light-chain] kinase
myosin light chain kinase
myosin-light-chain kinase
myosin light chain protein kinase
myosin light-chain kinase (phosphorylating)
ATP:myosin-light-chain O-phosphotransferase
smooth-muscle-myosin-light-chain kinase
calcium/calmodulin-dependent myosin light chain kinase
MLCK
MLCKase
STK18
myosin kinase
13. 2.7.1.117 enzyme myosin-light-chain kinase
myosin light chain protein kinase
myosin light-chain kinase (phosphorylating)
ATP:[myosin-light-chain] O-phosphotransferase
ATP:myosin-light-chain O-phosphotransferase
smooth-muscle-myosin-light-chain kinase
calcium/calmodulin-dependent myosin light chain kinase
myosin kinase
14. 2.7.1.129 enzyme [myosin-heavy-chain] kinase
myosin-heavy-chain kinase
ATP:[myosin-heavy-chain] O-phosphotransferase
ATP:myosin-heavy-chain O-phosphotransferase
15. 3.1.3.53 enzyme [myosin-light-chain] phosphatase
myosin-light-chain-phosphatase
[myosin-light-chain]-phosphate phosphohydrolase
myosin light chain kinase phosphatase
myosin phosphatase
protein phosphatase 2A
16. 4.1.1.72 enzyme branched-chain keto acid decarboxylase
branched-chain oxo acid decarboxylase
branched-chain-2-oxoacid decarboxylase
branched-chain alpha-keto acid decarboxylase
BCKA
(3S)-3-methyl-2-oxopentanoate carboxy-lyase
17. 5.3.1.21 enzyme corticosteroid side-chain-isomerase
11-deoxycorticosterone ketol-isomerase
11-deoxycorticosterone aldose-ketose-isomerase
18. 1.11.1.3 enzyme long chain fatty acid peroxidase
fatty-acid peroxidase
hexadecanoate:hydrogen-peroxide oxidoreductase
19. 1.1.1.211 enzyme long-chain-3-hydroxyacyl-CoA dehydrogenase
long-chain 3-hydroxyacyl coenzyme A dehydrogenase
long-chain-(S)-3-hydroxyacyl-CoA:NAD+ oxidoreductase
LCHAD
3-hydroxyacyl-CoA dehydrogenase
beta-hydroxyacyl-CoA dehydrogenase
20. 1.2.7.7 enzyme branched-chain ketoacid ferredoxin reductase
branched-chain oxo acid ferredoxin reductase
VOR
ketoisovalerate ferredoxin reductase
2-ketoisovalerate ferredoxin reductase
2-oxoisovalerate ferredoxin reductase
keto-valine-ferredoxin oxidoreductase
3-methyl-2-oxobutanoate dehydrogenase (ferredoxin)
3-methyl-2-oxobutanoate synthase (ferredoxin)
3-methyl-2-oxobutanoate:ferredoxin oxidoreductase (decarboxylating; CoA-2-methylpropanoylating)
21. 1.3.99.12 enzyme branched-chain acyl-CoA dehydrogenase
2-methyl branched chain acyl-CoA dehydrogenase
2-methylacyl-CoA dehydrogenase
2-methylbutanoyl-CoA:(acceptor) oxidoreductase
22. 1.3.99.13 enzyme long-chain-acyl-CoA dehydrogenase
long-chain acyl-coenzyme A dehydrogenase
long-chain-acyl-CoA:(acceptor) 2,3-oxidoreductase
palmitoyl-CoA dehydrogenase
palmitoyl-coenzyme A dehydrogenase
23. 1.3.99.2 enzyme short-chain acyl CoA dehydrogenase
short-chain acyl-coenzyme A dehydrogenase
butyryl dehydrogenase
ethylene reductase
butyryl-CoA dehydrogenase
3-hydroxyacyl CoA reductase
butyryl coenzyme A dehydrogenase
enoyl-coenzyme A reductase
unsaturated acyl-CoA reductase
unsaturated acyl coenzyme A reductase
butanoyl-CoA:(acceptor) 2,3-oxidoreductase
24. 1.3.99.3 enzyme long-chain acyl-CoA dehydrogenase
medium-chain acyl-CoA dehydrogenase
long-chain acyl coenzyme A dehydrogenase
medium-chain acyl-coenzyme A dehydrogenase
acyl dehydrogenase
acyl CoA dehydrogenase
acyl-CoA dehydrogenase
acyl coenzyme A dehydrogenase
fatty-acyl-CoA dehydrogenase
general acyl CoA dehydrogenase
fatty acyl coenzyme A dehydrogenase
acyl-CoA:(acceptor) 2,3-oxidoreductase
25. 2.3.1.16 enzyme long-chain 3-oxoacyl-CoA thiolase
KAT
3-ketothiolase
beta-ketothiolase
thiolase I
3-ketoacyl thiolase
acetyl-CoA acyltransferase
ketoacyl-CoA acyltransferase
3-ketoacyl CoA thiolase
3-ketoacyl-CoA thiolase
3-oxoacyl-CoA thiolase
6-oxoacyl-CoA thiolase
acetoacetyl-CoA beta-ketothiolase
acetyl-CoA C-acyltransferase
beta-ketoacyl-CoA thiolase
beta-ketoadipyl-CoA thiolase
ketoacyl-coenzyme A thiolase
oxoacyl-coenzyme A thiolase
2-methylacetoacetyl-CoA thiolase [misleading]
3-ketoacyl coenzyme A thiolase
3-oxoacyl-coenzyme A thiolase
beta-ketoacyl coenzyme A thiolase
beta-ketoadipyl coenzyme A thiolase
pro-3-ketoacyl-CoA thiolase
acyl-CoA:acetyl-CoA C-acyltransferase
26. 2.3.1.75 enzyme long-chain-alcohol O-fatty-acyltransferase
acyl-CoA:long-chain-alcohol O-acyltransferase
wax synthase
wax-ester synthase
27. 2.7.2.14 enzyme branched-chain-fatty-acid kinase
ATP:branched-chain-fatty-acid 1-phosphotransferase
isobutyrate kinase
28. 3.1.1.28 enzyme long-chain acyl-L-carnitine hydrolase
HACH
acylcarnitine hydrolase
palmitoylcarnitine hydrolase
O-acylcarnitine acylhydrolase
carnitine ester hydrolase
palmitoyl carnitine hydrolase
high activity acylcarnitine hydrolase
palmitoyl-L-carnitine hydrolase
29. 3.1.2.18 enzyme short-chain acyl-CoA hydrolase
short-chain acyl-CoA thioesterase
short-chain acyl coenzyme A hydrolase
ADP-dependent short-chain-acyl-CoA hydrolase
ADP-dependent-short-chain-acyl-CoA hydrolase
propionyl-CoA hydrolase
propionyl-CoA thioesterase
propionyl coenzyme A hydrolase
30. 3.5.1.60 enzyme N-(long-chain-acyl)ethanolamine amidohydrolase
N-(long-chain-acyl)ethanolamine deacylase
acylethanolamine amidase
N-acylethanolamine amidohydrolase
31. 4.2.1.17 enzyme short-chain enoyl-CoA hydratase
short chain enoyl coenzyme A hydratase
ECH
crotonase
crotonyl hydrase
enoyl hydrase
beta-hydroxyacid dehydrase
enol-CoA hydratase
enoyl-CoA hydratase
2-enoyl-CoA hydratase
acyl coenzyme A hydrase
beta-hydroxyacyl-CoA dehydrase
enoyl coenzyme A hydratase
hydratase, enoyl coenzyme A
unsaturated acyl-CoA hydratase
2-octenoyl coenzyme A hydrase
D-3-hydroxyacyl-CoA dehydratase
enoyl coenzyme A hydrase (D)
enoyl coenzyme A hydrase (L)
trans-2-enoyl-CoA hydratase
(3S)-3-hydroxyacyl-CoA hydro-lyase
32. 4.2.1.74 enzyme long-chain-enoyl-CoA hydratase
long-chain enoyl coenzyme A hydratase
long-chain-(3S)-3-hydroxyacyl-CoA hydro-lyase
33. 6.2.1.1 enzyme short chain fatty acyl-CoA synthetase
short-chain acyl-coenzyme A synthetase
ACS
acetate thiokinase
acetic thiokinase
acetate-CoA ligase
acetyl CoA ligase
acetyl CoA synthase
acetyl activating enzyme
acetyl-CoA synthetase
acyl-activating enzyme
acetyl coenzyme A synthetase
acetyl-coenzyme A synthase
acetate:CoA ligase (AMP-forming)
34. 6.2.1.2 enzyme fatty acid thiokinase (medium chain)
medium chain acyl-CoA synthetase
short-chain acyl-CoA synthetase
acyl-activating enzyme
butyrate-CoA ligase
butyryl-CoA synthetase
fatty acid elongase
butyryl-coenzyme A synthetase
fatty acid activating enzyme
L-(+)-3-hydroxybutyryl CoA ligase
butanoate:CoA ligase (AMP-forming)
fatty acyl coenzyme A synthetase
35. 6.2.1.3 enzyme fatty acid thiokinase (long chain)
long-chain acyl CoA synthetase
long chain fatty acyl-CoA synthetase
long-chain acyl-CoA synthetase I
long-chain acyl-CoA synthetase II
long-chain acyl-coenzyme A synthetase
long-chain-fatty-acid-CoA ligase
long-chain fatty acyl coenzyme A synthetase
ACS3
FAA1
thiokinase
LCFA synthetase
acyl-CoA ligase
acyl-CoA synthetase
acyl-activating enzyme
arachidonyl-CoA synthetase
fatty acid elongase
lignoceroyl-CoA synthase
oleoyl-CoA synthetase
palmitoyl-CoA ligase
palmitoyl-CoA synthase
pristanoyl-CoA synthetase
stearoyl-CoA synthetase
acyl coenzyme A synthetase
acyl-coenzyme A ligase
fatty acid CoA ligase
palmitoyl coenzyme A synthetase
acid:CoA ligase (AMP-forming)
fatty acyl-coenzyme A synthetase
36. 1.14.19.3 enzyme long-chain fatty acid delta6-desaturase
delta6-desaturase
linoleate desaturase
linoleic desaturase
linoleic acid desaturase
linoleoyl CoA desaturase
linoleoyl-CoA desaturase
delta6-acyl CoA desaturase
fatty acid 6-desaturase
fatty acid delta6-desaturase
linoleoyl-coenzyme A desaturase
delta6-fatty acyl-CoA desaturase
linoleoyl-CoA,hydrogen-donor:oxygen oxidoreductase
37. 1.2.1.50 enzyme long-chain-fatty-acyl-CoA reductase
long-chain-aldehyde:NADP+ oxidoreductase (acyl-CoA-forming)
acyl-CoA reductase
acyl coenzyme A reductase
38. 1.3.1.52 enzyme 2-methyl-branched-chain-enoyl-CoA reductase
2-methyl-branched-chain-acyl-CoA:NAD+ 2-oxidoreductase
39. 2.7.1.115 enzyme branched-chain alpha-ketoacid dehydrogenase kinase
branched-chain keto acid dehydrogenase kinase
branched-chain 2-oxo acid dehydrogenase kinase
branched-chain oxo acid dehydrogenase kinase (phosphorylating)
[3-methyl-2-oxobutanoate dehydrogenase (lipoamide)] kinase
ATP:[3-methyl-2-oxobutanoate dehydrogenase (lipoamide)] phosphotransferase
40. 3.1.2.2 enzyme long-chain fatty-acyl-CoA hydrolase
palmitoyl thioesterase
palmityl thioesterase
palmitoyl-CoA deacylase
palmitoyl-CoA hydrolase
palmitoyl-CoA hydrolase
palmityl thioesterase I
palmityl-CoA deacylase
fatty acyl thioesterase I
palmitoyl coenzyme A hydrolase
41. 3.1.3.52 enzyme branched-chain oxo-acid dehydrogenase phosphatase
branched-chain 2-keto acid dehydrogenase phosphatase
branched-chain alpha-keto acid dehydrogenase phosphatase
BCKDH
[3-methyl-2-oxobutanoate dehydrogenase (lipoamide)]-phosphatase
[3-methyl-2-oxobutanoate dehydrogenase (lipoamide)]-phosphate phosphohydrolase
42. 3.4.21.73 enzyme double-chain urokinase-type plasminogen activator
two-chain urokinase-type plasminogen activator
abbokinase
uPA
urokinase
u-PA
cellular plasminogen activator
u-plasminogen activator
urinary esterase A
urinary plasminogen activator
urokinase plasminogen activator
urokinase-type plasminogen activator
43. 1.1.1.36 enzyme short chain beta-ketoacetyl(acetoacetyl)-CoA reductase
acetoacetyl-CoA reductase
NADPH:acetoacetyl-CoA reductase
acetoacetyl coenzyme A reductase
beta-ketoacyl-CoA reductase
hydroxyacyl coenzyme-A dehydrogenase
(R)-3-hydroxyacyl-CoA dehydrogenase
D-3-hydroxyacyl-CoA reductase
NADP-linked acetoacetyl CoA reductase
(R)-3-hydroxyacyl-CoA:NADP+ oxidoreductase
D(-)-beta-hydroxybutyryl CoA-NADP oxidoreductase
44. 3.1.1.67 enzyme long-chain-fatty-acyl-ethyl-ester acylhydrolase
FAEES
fatty-acyl-ethyl-ester synthase
45. 3.1.3.16 enzyme branched-chain alpha-keto acid dehydrogenase phosphatase
calcineurin
BCKDH phosphatase
casein phosphatase
phosphatase 2A
phosphatase 2B
phosphatase I
phosphatase IB
phosphatase II
phosphatase III
phosphatase IV
phosphatase SP
phosphoprotein phosphatase
phosphoprotein phosphohydrolase
phosphospectrin phosphatase
protein phosphatase
phosphatase C-II
phosphatase H-II
phosphopyruvate dehydrogenase phosphatase
protein D phosphatase
protein phosphatase-1
protein phosphatase-2A
protein phosphatase-2B
protein phosphatase-2C
HMG-CoA reductase phosphatase
polycation modulated (PCM-) phosphatase
Aspergillus awamori acid protein phosphatase
3-hydroxy 3-methylglutaryl coenzymeA reductase phosphatase
46. 6.2.1.19 enzyme long-chain-fatty-acid-luciferin-component ligase
long-chain-fatty-acid:protein ligase (AMP-forming)
acyl-protein synthetase
47. 2.5.1.26 enzyme 1-acyl-glycerone-3-phosphate:long-chain-alcohol O-3-phospho-2-oxopropanyltransferase
DHAP-AT
alkyl-DHAP
alkyldihydroxyacetonephosphate synthase
alkyl DHAP synthetase
alkyldihydroxyacetone phosphate synthetase
alkylglycerone-phosphate synthase
dihydroxyacetone-phosphate acyltransferase
48. 6.2.1.20 enzyme long-chain-fatty-acid-[acyl-carrier-protein] ligase
long-chain-fatty-acid:[acyl-carrier-protein] ligase (AMP-forming)
acyl-ACP synthetase
stearoyl-ACP synthetase
acyl-[acyl carrier protein] synthetase
acyl-[acyl-carrier-protein] synthetase
acyl-[acyl-carrier-protein]synthetase
acyl-acyl carrier protein synthetase
49. 1.14.13.54 enzyme 17alpha-hydroxyprogesterone, NADPH2:oxygen oxidoreductase (20-hydroxylating, side-chain cleaving)
ketosteroid,NADPH:oxygen oxidoreductase (20-hydroxylating, ester-producing/20-hydroxylating, side-chain cleaving/17-hydroxylating, lactonizing)
ketosteroid monooxygenase
steroid-ketone monooxygenase
androstenedione, NADPH2:oxygen oxidoreductase (17-hydroxylating, lactonizing)
progesterone, NADPH2:oxygen oxidoreductase (20-hydroxylating, ester-producing)
BiSSCat v1.06.20 http://bisscat.org/
Developed by Masaaki Kotera, Department of Biochemistry, Trinity College Dublin.
Science Foundation of Ireland is gratefully acknowledged.