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Home Help FGROUP SUBSTRUCTURE compound enzyme Multiple

EC 1.14.11.1 gamma-butyrobetaine dioxygenase

IUBMB ExplorEnz BRENDA KEGG ExPASy ERGO

Equation(s) (IUBMB)

4-trimethylammoniobutanoate + 2-oxoglutarate + O2 = 3-hydroxy-4-trimethylammoniobutanoate + succinate + CO2

Reaction(s) (KEGG)

R02397 [Fig]4-Trimethylammoniobutanoate + 2-Ketoglutaric acid + O2 <=>3-Hydroxy-4-trimethylammoniobutanoate + Butanedionic acid + CO2
R02399 [Fig]3-Dehydroxycarnitine <=>3-Hydroxy-4-trimethylammoniobutanoate

Cofactor(s)

Iron
Vitamin C

BiSSCat v1.06.20 http://bisscat.org/
Developed by Masaaki Kotera, Department of Biochemistry, Trinity College Dublin.
Science Foundation of Ireland is gratefully acknowledged.