- 2.1.3.1 methylmalonyl-CoA carboxytransferase
- 2.8.1.6 biotin synthase
- 3.5.1.12 biotinidase
- 4.1.1.3 oxaloacetate decarboxylase
- 6.2.1.11 biotin-CoA ligase
- 6.3.4.10 biotin-[propionyl-CoA-carboxylase (ATP-hydrolysing)] ligase
- 6.3.4.11 biotin-[methylcrotonoyl-CoA-carboxylase] ligase
- 6.3.4.15 biotin-[acetyl-CoA-carboxylase] ligase
- 6.3.4.6 urea carboxylase
- 6.3.4.9 biotin-[methylmalonyl-CoA-carboxytransferase] ligase
- 6.4.1.1 pyruvate carboxylase
- 6.4.1.2 acetyl-CoA carboxylase
- 6.4.1.3 propionyl-CoA carboxylase
- 6.4.1.4 methylcrotonoyl-CoA carboxylase
- 6.4.1.5 geranoyl-CoA carboxylase
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