Selected compound(s)
- C02636 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium
Each orphan metabolite is emphasized in bold.
Click [Fig] on the left hand, and the image of the reaction is shown.
[Suggested reactions |
Reported reactions]
Suggested reactions
- [Fig] 1.1.1.- : (S)-Carnitine + NAD+ = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + NADH + H+
- [Fig] 1.1.1.- : 3-Hydroxy-4-trimethylammoniobutanoate + NAD+ = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + NADH + H+
- [Fig] 1.1.1.- : 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + NADPH + H+ = (S)-Carnitine + NADP+
- [Fig] 1.1.1.- : 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + NADPH + H+ = 3-Hydroxy-4-trimethylammoniobutanoate + NADP+
- [Fig] 1.1.3.- : (S)-Carnitine + O2 = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + H2O2
- [Fig] 1.1.3.- : 3-Hydroxy-4-trimethylammoniobutanoate + O2 = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + H2O2
- [Fig] 1.1.4.- : 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + 1,4-Dithiothreitol = (S)-Carnitine + Oxidized dithiothreitol
- [Fig] 1.1.4.- : 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + 1,4-Dithiothreitol = 3-Hydroxy-4-trimethylammoniobutanoate + Oxidized dithiothreitol
- [Fig] 1.1.5.- : 3-Hydroxy-4-trimethylammoniobutanoate + Coenzyme F420 = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + Reduced coenzyme F420
- [Fig] 1.1.5.- : 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + Reduced thioredoxin = 3-Hydroxy-4-trimethylammoniobutanoate + Oxidized thioredoxin
- [Fig] 1.1.5.- : 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + CoQH2 = (S)-Carnitine + CoQ
- [Fig] 1.1.5.- : 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + CoQH2 = 3-Hydroxy-4-trimethylammoniobutanoate + CoQ
- [Fig] 1.1.99.- : (S)-Carnitine + FAD = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + FADH2
- [Fig] 1.1.99.- : (S)-Carnitine + Coenzyme F420 = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + Reduced coenzyme F420
- [Fig] 1.1.99.- : 3-Hydroxy-4-trimethylammoniobutanoate + FAD = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + FADH2
Reported reactions
- [Fig] EC 1.1.1.108 : 3-Hydroxy-4-trimethylammoniobutanoate + NAD+ = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + NADH + H+
- [Fig] EC 1.1.1.254 : (S)-Carnitine + NAD+ = 3-Carboxy-N,N,N-trimethyl-2-oxo-1-propanaminium + NADH + H+
GREP v1.0.2 http://bisscat.org/GREP/
Developed by Masaaki Kotera (2008), Department of Biochemistry, Trinity College Dublin.
Science Foundation of Ireland is gratefully acknowledged.